ABSTRACT

Piebaldism is a rare autosomal skin disease characterized by white forelock and white patches located on the forehead, central abdomen and chest, upper arms, lower extremities. It is important that piebaldism can be confused with Waardenburg syndrome that may be associated with pathologies such as vitiligo, deafness and heterochromia. Generally it is a benign, persistent skin and hair disease. The disease affects the lives of people socially. There is no effective treatment. We present a one year old patient who had typical white spots on abdomen and forehead since birth. Patient was considered as piebaldism according to the family history and typical clinical presentation. We present this case because of its rarity with the literature.